Atelosteogenesis type II
Atelosteogenesis, type II (AOII; MIM 256050) is a disorder caused by mutations in the diastrophic dysplasia sulfate transporter gene (DTDST/SLC26A2). AOII is invariably lethal with survival measured in months. AOII is characterized by severe micromelia, spinal abnormalities, talipes equinovarus and abducted thumbs and toes. It is also known as neonatal osseous dysplasia I. AOII phenotypically occupies an intermediate position between achondrogenesis, type 1B (ACG1B; MIM 600972) and diastrophic dysplasia (DTD; MIM 222600), two other disorders caused by mutations in DTDST.